Recombinant人GCSH protein (ab113856)

概述

  • 产品名称Recombinant人GCSH protein
  • 蛋白长度Full length protein

描述

  • 性质Recombinant
  • 来源Escherichia coli
  • 氨基酸序列
    • AccessionP23434
    • 种属Human
    • 序列MGSSHHHHHHSSGLVPRGSHMGSMSVRKFTEKHEWVTTENGIGTVGISNF AQEALGDVVYCSLPEVGTKLNKQDEFGALESVKAASELYSPLSGEVTEIN EALAENPGLVNKSCYEDGWLIKMTLSNPSELDELMSEEAYEKYIKSIEE
    • 分子量16 kDa including tags
    • 氨基酸49 to 173
    • 标签His tag N-Terminus

技术指标

Our Abpromise guarantee covers the use of ab113856 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

  • 应用

    Mass Spectrometry

    SDS-PAGE

  • 质谱法
    MALDI-TOF
  • 纯度> 95 % SDS-PAGE.
    ab113856 was purified using conventional chromatography techniques.
  • 形式Liquid
  • Concentration information loading...

制备和贮存

  • 稳定性和存储

    Shipped at 4°C. Store at +4°C short term (1-2 weeks). Upon delivery aliquot. Store at -20°C or -80°C. Avoid freeze / thaw cycle.

    pH: 8.00
    Constituents: 0.32% Tris HCl, 10% Glycerol, 0.02% DTT, 0.88% Sodium chloride

常规信息

  • 别名
    • GCE
    • GCSH
    • GCSH_HUMAN
    • Glycine cleavage system H protein
    • Glycine cleavage system H protein mitochondrial
    • Glycine cleavage system protein H
    • Glycine cleavage system protein H (aminomethyl carrier)
    • Lipoic acid containing protein
    • mitochondrial
    • Mitochondrial glycine cleavage system H protein
    • NKH
    see all
  • 功能The glycine cleavage system catalyzes the degradation of glycine. The H protein shuttles the methylamine group of glycine from the P protein to the T protein.
  • 疾病相关Defects in GCSH are a cause of non-ketotic hyperglycinemia (NKH) [MIM:605899]; also known as glycine encephalopathy (GCE). NKH is an autosomal recessive disease characterized by accumulation of a large amount of glycine in body fluid and by severe neurological symptoms.
  • 序列相似性Belongs to the gcvH family.
    Contains 1 lipoyl-binding domain.
  • 细胞定位Mitochondrion.
  • Information by UniProt

Recombinant Human GCSH protein 图像

  • 15% SDS-PAGE analysis of 3 µg ab113856.

Recombinant Human GCSH protein (ab113856)参考文献

ab113856 has not yet been referenced specifically in any publications.

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