产品名称 Recombinant人FBP1 protein 参阅全部 FBP1 蛋白酶
蛋白长度 Full length protein 描述
来源 Escherichia coli
序列 ab89244 is purified using conventional chromatography techniques. 技术指标
Abpromise guarantee covers the use of
in the following tested applications.
The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.
纯度 > 90
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Shipped at 4°C. Upon delivery aliquot and store at -20°C or -80°C. Avoid repeated freeze / thaw cycles.
Constituents: 10% Glycerol, 20mM Tris HCl, 1mM DTT, pH 8.0
6-bisphosphate 1-phosphohydrolase 1
D fructose 1 6 bisphosphate 1 phosphohydrolase 1
通路 Carbohydrate biosynthesis; gluconeogenesis.
疾病相关 Defects in FBP1 are the cause of fructose-1,6-bisphosphatase deficiency (FBPD) [MIM:229700]. FBPD is inherited as an autosomal recessive disorder mainly in the liver and causes life-threatening episodes of hypoglycemia and metabolic acidosis (lactacidemia) in newborn infants or young children.
序列相似性 Belongs to the FBPase class 1 family.
Information by UniProt
Recombinant Human FBP1 protein 图像
Recombinant Human FBP1 protein (ab89244)参考文献
has not yet been referenced specifically in any publications.
Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"