概述

  • 产品名称Anti-PDSS2抗体
    参阅全部 PDSS2 一抗
  • 描述
    兔多克隆抗体to PDSS2
  • 经测试应用适用于: WBmore details
  • 种属反应性
    与反应: Human
    预测可用于: Mouse, Rat, Cow, Pig
  • 免疫原

    Recombinant fragment, corresponding to a region within amino acids 88-321 of Human PDSS2 (NP_065114).

  • 阳性对照
    • A431 whole cell lysate

性能

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应用

Our Abpromise guarantee covers the use of ab96324 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

应用 Ab评论 说明
WB 1/500 - 1/3000. Predicted molecular weight: 44 kDa.

靶标

  • 功能Supplies decaprenyl diphosphate, the precursor for the side chain of the isoprenoid quinones ubiquinone-10.
  • 通路Cofactor biosynthesis; ubiquinone biosynthesis.
  • 疾病相关Defects in PDSS2 are a cause of coenzyme Q10 deficiency (COQ10D) [MIM:607426]. Coenzyme Q10 deficiency is an autosomal recessive disorder with variable manifestations. It can be associated with three main clinical phenotypes: a predominantly myopathic form with central nervous system involvement, an infantile encephalomyopathy with renal dysfunction and an ataxic form with cerebellar atrophy.
  • 序列相似性Belongs to the FPP/GGPP synthase family.
  • 细胞定位Mitochondrion.
  • Information by UniProt
  • 数据库链接
  • 别名
    • All-trans-decaprenyl-diphosphate synthase subunit 2 antibody
    • bA59I9.3 antibody
    • C6orf210 antibody
    • Candidate tumor suppressor protein antibody
    • chromosome 6 open reading frame 210 antibody
    • Decaprenyl pyrophosphate synthase subunit 2 antibody
    • decaprenyl pyrophosphate synthetase subunit 2 antibody
    • Decaprenyl-diphosphate synthase subunit 2 antibody
    • DLP1 antibody
    • DLP1_HUMAN antibody
    • hDLP1 antibody
    • Pdss2 antibody
    • prenyl (decaprenyl) diphosphate synthase, subunit 2 antibody
    • subunit 2 of decaprenyl diphosphate synthase antibody
    see all

Anti-PDSS2 antibody 图像

  • Anti-PDSS2 antibody (ab96324) at 1/1000 dilution + A431 whole cell lysate at 30 µg

    Predicted band size : 44 kDa

Anti-PDSS2 antibody (ab96324)参考文献

ab96324 has not yet been referenced specifically in any publications.

Product Wall

Abreviews
Application Western blot
Sample Mouse Cell lysate - other (Mouse heart Mitochondria-ab110350)
Gel Running Conditions Non-reduced Non-Denaturing (Native) (12%)
Loading amount 30 µg
Specification Mouse heart Mitochondria-ab110350
Blocking step Milk as blocking agent for 2 hour(s) and 0 minute(s) · Concentration: 0.05% · Temperature: RT°C
Username

Daniella Oxer

Verified customer

提交于 Apr 20 2015

Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"