概述

  • 产品名称
  • 描述
    小鼠多克隆抗体to PDSS2
  • 经测试应用
    适用于: WBmore details
  • 种属反应性
    与反应: Human
  • 免疫原

    Full-length Human PDSS2 (NP_065114)

  • 阳性对照
    • Human kidney tissue

性能

应用

Our Abpromise guarantee covers the use of ab88817 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

应用 Ab评论 说明
WB 1/500 - 1/1000. Predicted molecular weight: 44 kDa.

靶标

  • 功能
    Supplies decaprenyl diphosphate, the precursor for the side chain of the isoprenoid quinones ubiquinone-10.
  • 通路
    Cofactor biosynthesis; ubiquinone biosynthesis.
  • 疾病相关
    Defects in PDSS2 are a cause of coenzyme Q10 deficiency (COQ10D) [MIM:607426]. Coenzyme Q10 deficiency is an autosomal recessive disorder with variable manifestations. It can be associated with three main clinical phenotypes: a predominantly myopathic form with central nervous system involvement, an infantile encephalomyopathy with renal dysfunction and an ataxic form with cerebellar atrophy.
  • 序列相似性
    Belongs to the FPP/GGPP synthase family.
  • 细胞定位
    Mitochondrion.
  • Information by UniProt
  • 数据库链接
  • 别名
    • All-trans-decaprenyl-diphosphate synthase subunit 2 antibody
    • bA59I9.3 antibody
    • C6orf210 antibody
    • Candidate tumor suppressor protein antibody
    • chromosome 6 open reading frame 210 antibody
    • Decaprenyl pyrophosphate synthase subunit 2 antibody
    • decaprenyl pyrophosphate synthetase subunit 2 antibody
    • Decaprenyl-diphosphate synthase subunit 2 antibody
    • DLP1 antibody
    • DLP1_HUMAN antibody
    • hDLP1 antibody
    • Pdss2 antibody
    • prenyl (decaprenyl) diphosphate synthase, subunit 2 antibody
    • subunit 2 of decaprenyl diphosphate synthase antibody
    see all

Anti-PDSS2 antibody 图像

  • Anti-PDSS2 antibody (ab88817) at 1/500 dilution + Human kidney tissue lysate at 50 µg

    Predicted band size : 44 kDa
    Observed band size : 44 kDa
  • All lanes : Anti-PDSS2 antibody (ab88817) at 1/500 dilution

    Lane 1 : transfected 293T cell lysate
    Lane 2 : untransfected 293T cell lysate

    Lysates/proteins at 25 µg per lane.


    Predicted band size : 44 kDa
    Observed band size : 44 kDa

实验方案

Anti-PDSS2 antibody (ab88817)参考文献

ab88817 has not yet been referenced specifically in any publications.

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