Anti-Nucleotide binding protein like抗体(ab69150)

概述

性能

  • 形式Liquid
  • 存放说明Shipped at 4°C. Upon delivery aliquot and store at -20°C or -80°C. Avoid repeated freeze / thaw cycles.
  • 存储溶液Preservative: None
    Constituents: 1X PBS, pH 7.2
  • Concentration information loading...
  • 纯度Protein G purified
  • 克隆多克隆
  • 同种型IgG
  • 研究领域

应用

Our Abpromise guarantee covers the use of ab69150 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

应用 Ab评论 说明
WB 1/500 - 1/1000. Predicted molecular weight: 34 kDa.

靶标

  • 功能Required for the assembly of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I). May deliver of one or more Fe-S clusters to complex I subunits.
  • 组织特异性Highest expression in liver and kidney. expressed at significant levels in small intestine and brain (at protein level).
  • 疾病相关Defects in NUBPL are a cause of mitochondrial complex I deficiency (MT-C1D) [MIM:252010]. A disorder of the mitochondrial respiratory chain that causes a wide range of clinical manifestations from lethal neonatal disease to adult-onset neurodegenerative disorders. Phenotypes include macrocephaly with progressive leukodystrophy, non-specific encephalopathy, cardiomyopathy, myopathy, liver disease, Leigh syndrome, Leber hereditary optic neuropathy, and some forms of Parkinson disease.
  • 序列相似性Belongs to the Mrp/NBP35 ATP-binding proteins family.
  • 细胞定位Mitochondrion.
  • Information by UniProt
  • 数据库链接
  • 别名
    • C14orf127 antibody
    • FLJ12660 antibody
    • huInd1 antibody
    • IND1 homolog antibody
    • Iron-sulfur protein NUBPL antibody
    • Nubpl antibody
    • NUBPL_HUMAN antibody
    • nucleotide binding protein like antibody
    • Nucleotide-binding protein-like antibody
    see all

Anti-Nucleotide binding protein like antibody (ab69150)参考文献

ab69150 has not yet been referenced specifically in any publications.

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