概述

描述

  • 性质Synthetic
  • 氨基酸序列
    • 种属Human
    • 序列TILTYPFKNLPT-C
    • 氨基酸2 to 13

相关产品

技术指标

Our Abpromise guarantee covers the use of ab23180 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

  • 应用

    Blocking - Blocking peptide for Anti-HADHB antibody (ab10093)

  • 形式Liquid
  • Concentration information loading...

制备和贮存

  • 稳定性和存储

    Shipped at 4°C. Upon delivery aliquot and store at -20°C or -80°C. Avoid repeated freeze / thaw cycles.

常规信息

  • 别名
    • 2 enoyl Coenzyme A (CoA) hydratase beta subunit
    • 3 ketoacyl Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein beta subunit
    • 3 ketoacyl Coenzyme A thiolase
    • 3 ketoacyl Coenzyme A thiolase of mitochondrial trifunctional protein beta subunit
    • 3-ketoacyl-CoA thiolase
    • Acetyl CoA acyltransferase
    • Acetyl-CoA acyltransferase
    • Beta ketothiolase
    • Beta-ketothiolase
    • ECHB
    • ECHB_HUMAN
    • HADH
    • Hadhb
    • Hydroxyacyl CoA dehydrogenase/3 ketoacyl CoA thiolase/enoyl CoA hydratase (trifunctional protein), beta subunit
    • Hydroxyacyl Coenzyme A (CoA) dehydrogenase beta subunit
    • Hydroxyacyl Coenzyme A dehydrogenase
    • Hydroxyacyl Coenzyme A dehydrogenase beta subunit
    • Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) beta subunit
    • MGC87480
    • Mitochondrial trifunctional enzyme beta subunit
    • Mitochondrial trifunctional protein beta subunit
    • MSTP 029
    • MSTP029
    • MTPB
    • TP beta
    • TP-beta
    • TPbeta
    • Trifunctional enzyme subunit beta
    • Trifunctional enzyme subunit beta mitochondrial
    • Trifunctional protein
    see all
  • 通路Lipid metabolism; fatty acid beta-oxidation.
  • 疾病相关Defects in HADHB are a cause of trifunctional protein deficiency (TFP deficiency) [MIM:609015]. The clinical manifestations are very variable and include hypoglycemia, cardiomyopathy and sudden death. Phenotypes with mainly hepatic and neuromyopathic involvement can also be distinguished. Biochemically, TFP deficiency is defined by the loss of all three enzyme activities of the TFP complex.
  • 序列相似性Belongs to the thiolase family.
  • 细胞定位Mitochondrion.
  • Information by UniProt

Human HADHB peptide (ab23180)参考文献

ab23180 has not yet been referenced specifically in any publications.

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