概述

  • 产品名称Anti-HPS6抗体
    参阅全部 HPS6 一抗
  • 描述
    兔多克隆抗体to HPS6
  • 经测试应用适用于: WBmore details
  • 种属反应性
    与反应: Human
  • 免疫原

    Amino acids 405-466 of Human HPS6 (NP_079023)

    EEACGYYQRRSLRGAQLTPEELRHSSTFRAPQALASILQGHLPPSALLTM LRTELRDYRGLE

  • 阳性对照
    • H1299, HeLa and HepG2 cell lines. A431 whole cell lysate.

性能

  • 形式Liquid
  • 存放说明Shipped at 4°C. Upon delivery aliquot. Store at -20°C or -80°C. Avoid freeze / thaw cycle.
  • 存储溶液Preservative: 0.01% Thimerosal (merthiolate)
    Constituents: 10% Glycerol, 0.1M Tris, 0.1M Glycine, pH 7.0
  • Concentration information loading...
  • 纯度Immunogen affinity purified
  • 克隆多克隆
  • 同种型IgG
  • 研究领域

相关产品

应用

Our Abpromise guarantee covers the use of ab96656 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

应用 Ab评论 说明
WB 1/1000. Predicted molecular weight: 83 kDa.

靶标

  • 功能May regulate the synthesis and function of lysosomes and of highly specialized organelles, such as melanosomes and platelet dense granules.
  • 组织特异性Ubiquitous.
  • 疾病相关Defects in HPS6 are the cause of Hermansky-Pudlak syndrome type 6 (HPS6) [MIM:614075]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.
  • 细胞定位Microsome membrane. Cytoplasm > cytosol. Early endosome membrane.
  • Information by UniProt
  • 数据库链接
  • 别名
    • FLJ22501 antibody
    • Hermansky Pudlak syndrome 6 protein antibody
    • Hermansky-Pudlak syndrome 6 protein antibody
    • HPS6 antibody
    • HPS6_HUMAN antibody
    • MGC20522 antibody
    • Ru antibody
    • Ruby eye protein homolog antibody
    • Ruby-eye protein homolog antibody
    see all

Anti-HPS6 antibody 图像

  • Anti-HPS6 antibody (ab96656) at 1/1000 dilution + A431 whole cell lysate at 30 µg

    Predicted band size : 83 kDa

Anti-HPS6 antibody (ab96656)参考文献

ab96656 has not yet been referenced specifically in any publications.

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