概述

  • 产品名称Anti-ETFDH抗体
    参阅全部 ETFDH 一抗
  • 描述
    山羊多克隆抗体to ETFDH
  • 经测试应用适用于: WBmore details
  • 种属反应性
    与反应: Mouse, Rat, Human
    预测可用于: Rabbit, Cow, Dog, Pig, Zebrafish, Orangutan
  • 免疫原

    Synthetic peptide:

    C-EHDQPAHLTLRD

    , corresponding to internal sequence amino acids 530-541 of Human ETFDH (NP_004444.2).

  • 阳性对照
    • Human, Mouse and Rat Heart lysates, Human kidney lysate.

性能

应用

Our Abpromise guarantee covers the use of ab103910 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

应用 Ab评论 说明
WB Use a concentration of 1 - 3 µg/ml. Predicted molecular weight: 69 kDa.

靶标

  • 功能Accepts electrons from ETF and reduces ubiquinone.
  • 疾病相关Defects in ETFDH are the cause of glutaric aciduria type 2C (GA2C) [MIM:231680]. GA2C is an autosomal recessively inherited disorder of fatty acid, amino acid, and choline metabolism. It is characterized by multiple acyl-CoA dehydrogenase deficiencies resulting in large excretion not only of glutaric acid, but also of lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids.
  • 序列相似性Belongs to the ETF-QO/fixC family.
    Contains 1 4Fe-4S ferredoxin-type domain.
  • 细胞定位Mitochondrion inner membrane.
  • Information by UniProt
  • 数据库链接
  • 别名
    • Electron transfer flavoprotein ubiquinone oxidoreductase antibody
    • Electron transfer flavoprotein-ubiquinone oxidoreductase antibody
    • electron transferring flavoprotein dehydrogenase antibody
    • Electron-transferring-flavoprotein dehydrogenase antibody
    • ETF dehydrogenase antibody
    • ETF QO antibody
    • ETF ubiquinone oxidoreductase antibody
    • ETF-QO antibody
    • ETF-ubiquinone oxidoreductase antibody
    • ETFD_HUMAN antibody
    • Etfdh antibody
    • mitochondrial antibody
    see all

Anti-ETFDH antibody 图像

Anti-ETFDH antibody (ab103910)参考文献

ab103910 has not yet been referenced specifically in any publications.

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