Anti-Cytochrome C Oxidase subunit VIb抗体(ab96692)

概述

  • 产品名称Anti-Cytochrome C Oxidase subunit VIb抗体
    参阅全部 Cytochrome C Oxidase subunit VIb 一抗
  • 描述
    兔多克隆抗体to Cytochrome C Oxidase subunit VIb
  • 经测试应用适用于: WBmore details
  • 种属反应性
    与反应: Human
    预测可用于: Monkey
  • 免疫原

    Synthetic peptide, corresponding to a sequence within amino acids 23-86 of Human Cytochrome C Oxidase subunit VIb (NP_001854).

  • 阳性对照
    • A431, HeLa cell lysates and HepG2 whole cell lysate.

性能

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应用

Our Abpromise guarantee covers the use of ab96692 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

应用 Ab评论 说明
WB 1/500 - 1/3000. Predicted molecular weight: 10 kDa.

靶标

  • 功能Connects the two COX monomers into the physiological dimeric form.
  • 疾病相关Defects in COX6B1 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110]; also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.
  • 序列相似性Belongs to the cytochrome c oxidase subunit 6B family.
  • 细胞定位Mitochondrion intermembrane space.
  • Information by UniProt
  • 数据库链接
  • 别名
    • COX 6B antibody
    • COX VIb 1 antibody
    • COX VIb-1 antibody
    • COX6B antibody
    • COX6B1 antibody
    • COXG antibody
    • COXVIb1 antibody
    • CX6B1_HUMAN antibody
    • Cytochrome c oxidase subunit 6B1 antibody
    • Cytochrome c oxidase subunit VIb antibody
    • Cytochrome c oxidase subunit VIb isoform 1 antibody
    • cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody
    • Cytochrome c oxidase subunit Vib polypeptide 1 antibody
    see all

Anti-Cytochrome C Oxidase subunit VIb antibody 图像

  • Anti-Cytochrome C Oxidase subunit VIb antibody (ab96692) at 1/1000 dilution + HepG2 whole cell lysate at 30 µg

    Predicted band size : 10 kDa

Anti-Cytochrome C Oxidase subunit VIb antibody (ab96692)参考文献

ab96692 has not yet been referenced specifically in any publications.

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