存放说明 Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.
存储溶液 Preservative: 0.02% Sodium Azide
Constituents: 50% Glycerol, Whole serum, Tris buffered saline, 0.5mg/ml BSA, pH 7.4
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纯度 Protein A purified
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in the following tested applications.
The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.
1/200. Predicted molecular weight: 43 kDa.
功能 This enzyme is specific for acyl chain lengths of 4 to 16.
通路 Lipid metabolism; mitochondrial fatty acid beta-oxidation.
疾病相关 Defects in ACADM are the cause of acyl-CoA dehydrogenase medium-chain deficiency (ACADMD) [MIM:201450]. It is an autosomal recessive disease which causes fasting hypoglycemia, hepatic dysfunction, and encephalopathy, often resulting in death in infancy.
序列相似性 Belongs to the acyl-CoA dehydrogenase family.
细胞定位 Mitochondrion matrix.
Information by UniProt
ACAD 1 antibody
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